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1,6-二磷酸果糖一鈣鹽號：103213-33-8   
英文名稱：FDPCa；D-Fructose-1,6-diphoshate calcium salt   
其他名稱：1,6-二磷酸左旋糖一鈣鹽；D-果糖-1,6-二磷酸一鈣鹽；果糖-1,6-二磷酸一鈣鹽；D-果糖-1,6-二磷酸鈣鹽   
號：103213-33-8   
C6H12CaO12P2=378.18   
級別：BR   
含量：≥85%   
重金屬：≤20ppm   
性狀(以下信息僅供參考)：白色或黃色粉末   
用途：本品僅供科研，不得用于其它用途   
保存：2～8℃1,6-二磷酸果糖一鈣鹽號：103213-33-8儲存條件：
避光、干燥陰涼處封閉貯存,嚴禁與有毒、有害物品混放、混運。本品為非危險 產(chǎn)品可按一般化學品運輸,輕搬動輕放,防止日曬、雨淋！受熱、受潮、受光后易喪失活力,保存期短,因此貯存和運輸條件比較苛刻。
運輸：汽車運輸、EMS郵政快遞，申通快遞等， 款到上海3天內(nèi)發(fā)貨；
售后：如您對我們的產(chǎn)品服務(wù)及技術(shù)指標有特殊要求，請及時通知我方。
存儲：應(yīng)貯存在干燥清潔避光的環(huán)境中，嚴禁與有毒物質(zhì)混放，以免污染（保質(zhì)期為兩年）。
1,6-二磷酸果糖一鈣鹽號：103213-33-8主要優(yōu)級純、分級純和化學純3種：
（1）優(yōu)級純（GR：Guaranteed reagent），又稱一級品或保證試劑，99.8%，這種試劑純度Z高，雜質(zhì)含量Z低，適合于重要精密的分析工作和科學研究工作，使用綠色瓶簽。
（2）分析純（AR），又稱二級試劑，純度很高，99.7%，略次于優(yōu)級純，適合于重要分析及一般研究工作，使用紅色瓶簽。
（3）化學純（CP），又稱三級試劑，≥ 99.5%，純度與分析純相差較大，適用于工礦、學校一般分析工作。使用藍色（深藍色）標簽。
（4）實驗試劑（LR：Laboratory reagent），又稱四級試劑。

 not yet tested in other applications.
 optimal dilutions/concentrations should be determined by the end user. 
保存條件  Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Important Note  This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
產(chǎn)品介紹 Paraplegin is a 795 amino acid metalloprotease that is a member of the AAA protein family. Localized to the mitochrondrial membrane and expressed throughout the body, Paraplegin is a multi-pass membrane protein that is thought to be involved in signal transduction and chaperone-like activities in the mitochrondria. Defects in the gene encoding Paraplegin are the cause of spastic paraplegia type 7 (SPG7), a form of autosomal recessive hereditary spastic paraplegia (AR-HSP). HSPs are degenerative spinal cord disorders that are characterized by muscle spasms, stiffness in the legs and, in some cases, incontinence. Recent studies suggest that SPG7 may be a mitochondrial-based disease, as mutations in the Paraplegin gene lead to ragged-red fibers, oxidase-negative fibers and intense succinate dehydrogenase-stained areas of the mitochrondria. These mitochondrial dysfunctions lead to axonal degeneration and impaired axonal transport, thus causing the neurodegeneration seen in HSPs.
Function : SPG7 is a metalloprotease protein that is a member of the AAA (ATPases associated with a variety of cellular activities) protein family. Members of this protein family share an ATPase domain and have roles in diverse cellular processes including membrane trafficking, intracellular motility, organelle biogenesis, protein folding, and proteolysis. Two transcript variants encoding distinct isoforms have been identified for this gene. Mutations associated with this gene cause autosomal recessive spastic paraplegia 7.
Subunit : Interacts with AFG3L2; the interaction is required forthe efficient assembly of mitochondrial complex I.
Subcellular Location : Mitochondrion membrane; Multi pass membrane protein.
Tissue Specificity : Ubiquitous.
DISEASE : Defects in SPG7 are the cause of spastic paraplegiaautosomal recessive type 7 (SPG7) [MIM:607259]. Spastic paraplegiais a degenerative spinal cord disorder characterized by a slow,gradual, progressive weakness and spasticity of the lower limbs.SPG7 is a complex form. Additional clinical features are cerebellarsyndrome, supranuclear palsy, and cognitive impairment,particularly disturbance of attention and executive functions.
Note=Defects in SPG7 may cause autosomal recessiveosteogenesis imperfecta (OI). Osteogenesis i1,6-二磷酸果糖一鈣鹽號：103213-33-8mperfecta defines agroup of connective tissue disorders characterized by bonefragility and low bone mass. Clinical features of SPG7-relatedosteogenesis imperfecta include recurrent fractures, mild bonedeformities, delayed tooth eruption, normal hearing and whitesclera.
Similarity : In the N-terminal section; belongs to the AAA ATPasefamily.
In the C-terminal section; belongs to the peptidaseM41 family.
Database links : UniProtKB/Swiss-Prot: Q9UQ90.2
英文名稱  Anti-SPTBN2/Beta III spectrin
中文名稱  非紅細胞血影腦蛋白β2/spectrin β III抗體
別    名  Beta III spectrin; Beta-III spectrin; SCA 5; SCA5; Spectrin beta chain brain 2; Spectrin beta non erythrocytic 2; Spectrin non erythroid beta chain 2; Spinocerebellar ataxia 5; SPTBN 2; Spectrin beta chain, non-erythrocytic 2; Beta-III spectrin; Spinocerebellar ataxia 5 protein; SPTN2_HUMAN.
濃    度  1mg/1ml
規(guī) 格  0.2ml/200μg
抗體來源  Rabbit 
克隆類型  polyclonal
交叉反應(yīng)  Human, Mouse, Rat  
產(chǎn)品類型  一抗   
研究領(lǐng)域  神經(jīng)生物學 信號轉(zhuǎn)導 細胞骨架 細胞外基質(zhì) 
蛋白分子量  predicted molecular weight: 35kDa
性    狀  Lyophilized or Liquid
免 疫 原  KLH conjugated synthetic peptide derived from human Beta III spectrin (121-220aa)
亞    型  IgG
純化方法  affinity purified by Protein A
儲 存 液  Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
產(chǎn)品應(yīng)用   WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500
（石蠟切片需做抗原修復）
 not yet tested in other applications.
 optimal dilutions/concentrations should be determined by the end user. 
保存條件  Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
Important Note  This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
產(chǎn)品介紹 Spectrin is an actin binding protein that is a major component of the plasma membrane skeleton. Spectrins function as membrane organizers and stabilizers by forming dimers, tetramers and higher polymers. Spectrin Alpha and spectrin Beta are present in erythrocytes, whereas spectrin Alpha II (also designated fodrin Alpha) and spectrin Beta I (also designated fodrin Beta) are present in other somatic cells. The spectrin tetramers in erythrocytes act as barriers to lateral diffusion, but spectrin dimers seem to lack this function. Spectrin Beta III is highly homologous to both spectrin Beta I and spectrin Beta II. Western blot analysis shows that spectrin Beta III migrates at a higher molecular mass than predicted in the kidney. Spectrin Beta III is highly expressed in brain, kidney, pancreas, and liver, and at lower levels in lung and placenta. Specifically, spectrin Beta III constitutes a major component of the Golgi and vesicular membrane skeletons.
Function : Probably plays an important role in neuronal membrane skeleton.
Subcellular Location : Cytoplasm, cytoskeleton. Cytoplasm, cell cortex.
Tissue Specificity : Highly expressed in brain, kidney, pancreas, and liver, and at lower levels in lung and placenta.
DISEASE : Defects in SPTBN2 are the cause of spinocerebellar ataxia type 5 (SCA5) [MIM:600224]. Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders. Patients show progressive incoordination of gait and often poor coordination of hands, speech and eye movements, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord. SCA5 is an autosomal dominant cerebellar ataxia (ADCA). It is a slowly progressive disorder with variable age at onset, ranging between 10 and 50 years.
Similarity : Belongs to the spectrin family.
Contains 2 CH (calponin-homology) domains.
Contains 1 PH domain.
Contains 17 spectrin repeats.
Database links : UniProtKB/Swiss-Prot: O15020.3
英文名稱  Anti-SULT4A1
中文名稱  腦磺基轉(zhuǎn)移酶樣蛋白4A1抗體
別    名  BR STL 1; Brain sulfotransferase like protein; Brain sulphotransferase like; BRSTL1; hBR STL 1; hBR STL; Nervous system cytosolic sulfotransferase; Nervous system sulfotransferase; NST; Sulfotransferase 4A1; Sulfotransferase family 4A member 1; Sulfotransferase related protein; SULTX3; ST4A1_HUMAN.
濃    度  1mg/1ml
規(guī) 格  0.2ml/200μg
抗體來源  Rabbit 
克隆類型  polyclonal
交叉反應(yīng)  Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Sheep